Dietary Compliance

If you are on a restricted diet, it is very important to adhere closely to the dietary recommendations made by the physician or registered dietitian. Even trace amounts of sucrose-containing or starch-containing foods may have adverse effects and produce symptoms in an individual diagnosed with Congenital Sucrase-Isomaltase Deficiency (CSID).

Any individual or group that has an influence on the diet of a child with CSID (parent, guardian, extended family member, school personnel, and childcare provider) should be educated about the importance of dietary compliance. No person should tease or coax an individual with CSID into just tasting or trying a food not on their safe-foods list.

A safe-foods list or a foods-to-avoid list can be a great benefit to the younger individual, teacher, grandparent, and friend who is not familiar with the dietary restrictions related to life with CSID. Your physician or registered dietitian may help you develop the best list for your personal dietary restrictions. At initial diagnosis, the safe-foods list may seem small, but with time, more foods may be added, depending on how well they are tolerated.

Maintaining wellness depends on strict compliance with dietary restrictions for both adults and children with CSID. Families of those with CSID may be told the diet is too difficult to manage, negatively impacting the family’s attitude toward the diet from the outset. Parents, siblings, and all persons in a child’s life should share a positive attitude toward compliance. This positive attitude enhances the child’s ability to cope with the pressures of strict diet adherence. Without making a big deal about the restrictions, a CSID-compliant diet should become part of the daily ritual of meal planning versus being treated like a chore or interference to normal mealtimes.

Using certain phrases for those who do not fully understand the impact of CSID may be helpful. A suggested explanation could be, “We all eat. Everyone eats. Some of us just need to eat differently to stay healthy.” CSID is a lifelong diagnosis and keeping symptoms to a minimum frees your or your child to live a typical daily life without worry.

IMPORTANT SAFETY INFORMATION FOR SUCRAID^® (SACROSIDASE) ORAL SOLUTION

Sucraid^® may cause a serious allergic reaction. If you notice any swelling or have difficulty breathing, get emergency help right away.
Tell your doctor if you are allergic to, have ever had a reaction to, or have ever had difficulty taking yeast, yeast products, papain, or glycerin (glycerol).
Sucraid^® does not break down some sugars that come from the digestion of starch. You may need to restrict the amount of starch in your diet. Your doctor will tell you if you should restrict starch in your diet.
Tell your doctor if you have diabetes, as your blood glucose levels may change if you begin taking Sucraid^®. Your doctor will tell you if your diet or diabetes medicines need to be changed.
Some patients treated with Sucraid^® may have worse abdominal pain, vomiting, nausea, or diarrhea. Constipation, difficulty sleeping, headache, nervousness, and dehydration have also occurred in patients treated with Sucraid^®. Check with your doctor if you notice these or other side effects.
Sucraid^® has not been tested to see if it works in patients with secondary (acquired) sucrase deficiency.
NEVER HEAT SUCRAID OR PUT IT IN WARM OR HOT BEVERAGES OR INFANT FORMULA. Do not mix Sucraid^® with fruit juice or take it with fruit juice. Take Sucraid® as prescribed by your doctor. Normally, half of the dose of Sucraid^® is taken before a meal or snack and the other half is taken during the meal or snack.
Sucraid^® should be refrigerated at 36°F-46°F (2°C-8°C) and should be protected from heat and light.

You are encouraged to report negative side effects of prescription drugs to the FDA. Visit www.FDA.gov/medwatch or call 1-800-FDA-1088.

INDICATION

Sucraid^® (sacrosidase) Oral Solution is an enzyme replacement therapy for the treatment of genetically determined sucrase deficiency, which is part of congenital sucrase-isomaltase deficiency (CSID).

Important Safety Information for Sucraid^® (sacrosidase) Oral Solution

Sucraid^® may cause a serious allergic reaction. If you notice any swelling or have difficulty breathing, get emergency help right away.
Tell your doctor if you are allergic to, have ever had a reaction to, or have ever had difficulty taking yeast, yeast products, papain, or glycerin (glycerol).
Sucraid^® does not break down some sugars that come from the digestion of starch. You may need to restrict the amount of starch in your diet. Your doctor will tell you if you should restrict starch in your diet.
Tell your doctor if you have diabetes, as your blood glucose levels may change if you begin taking Sucraid^®. Your doctor will tell you if your diet or diabetes medicines need to be changed.
Some patients treated with Sucraid^® may have worse abdominal pain, vomiting, nausea, or diarrhea. Constipation, difficulty sleeping, headache, nervousness, and dehydration have also occurred in patients treated with Sucraid^®. Check with your doctor if you notice these or other side effects.
Sucraid^® has not been tested to see if it works in patients with secondary (acquired) sucrase deficiency.
NEVER HEAT SUCRAID OR PUT IT IN WARM OR HOT BEVERAGES OR INFANT FORMULA. Do not mix Sucraid^® with fruit juice or take it with fruit juice. Take Sucraid® as prescribed by your doctor. Normally, half of the dose of Sucraid^® is taken before a meal or snack and the other half is taken during the meal or snack.
Sucraid^® should be refrigerated at 36°F-46°F (2°C-8°C) and should be protected from heat and light.

You are encouraged to report negative side effects of prescription drugs to the FDA. Visit www.FDA.gov/medwatch or call 1-800-FDA-1088.

Indication

Sucraid^® (sacrosidase) Oral Solution is an enzyme replacement therapy for the treatment of genetically determined sucrase deficiency, which is part of Congenital Sucrase-Isomaltase Deficiency (CSID).